Anetoderma or Macular atrophy is a rare cutaneous disorder showing local atrophy and macular discoloration related to a local dermal defect of elastic tissue without any other apparent change in the skin, which may show familial occurrence,
called
familial anetoderma.
A 13-year-old female complained 3-year history of multiple asymptomatic atrophic macules on the trunk and both lower extremities, especially on both thighs. Elastic stain of skin lesion showed decrease of elastic tissue in the dermis. No other
systemic
abnormalities were found on phisical examination. Her sister had same skin lesions on lower extremities and both buttocks. and had no other systemic abnormalities.
Despite infrequent occurrence, the development of anetoderma among familial members possibly represents a congenital defect of elastin. Because various ocular, bony, cardiac, and gastrointestinal abnormalities have been reported in familial
anetoderma,
long-term follow up would be necessary. (Kor J Dermatol 1992:30 (6) : 924-927)
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